January 2019 Vol. 7 No.1

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Case Report

Lingual alveolar sarcoma in children: a rare soft tissue sarcoma

Adil Fouad^1*, Meriem El Baz¹, Nadia Mansouri², Abderrachid Hamdaoui³, Dounia Basraoui⁴, Hicham Jalal⁴ and Jamila El Houdzy¹

¹Pediatric Hematology and Oncology Department, Mohammed VI University Hospital of Marrakesh, Morocco.
²Maxillofacial Department, Mohammed VI University Hospital of Marrakesh, Morocco.
³Center of Anathomocytopathology Zohor, Marrakesh, Morocco.
⁴Pediatric Radiology Department, Mohammed VI University Hospital of Marrakesh, Morocco.

*Corresponding Author’s E-mail: adilfouad@hotmail.fr
Tel /Fax: +212524300700

Accepted January 20, 2019

Abstract

Alveolar soft part sarcoma is a rare soft tissue sarcoma with a predilection for adolescents and young adults that tends to occur in the extremities. It is a well-differentiated and chemo-resistant solid tumor. Lingual alveolar sarcoma can occur at an early age and appears, in this case, to be chemo-sensitive. We report the case of a child with an ASPS of the tongue and the mouth floor with lung metastasis, never yet published in Morocco, and a review of the literature. Alveolar soft part sarcoma of the tongue and the mouth floor was diagnosed in a 13-year-old boy. He had a painful, occasionally bleeding, medio-lingual swelling, spanning the mouth floor and the pharynx, in progression for a year, complicated with dysphagia and dyspnea requiring emergency tracheotomy. He underwent a surgical excision of the mass, and then was treated by chemotherapy. The child died from hemorrhagic shock and worsening of the respiratory distress. ASPS should be included in the differential diagnosis of head and neck masses in children since early detection and treatment are essential. In particular, lingual alveolar sarcoma diagnosed at an early age seems to be chemo-sensitive.

Keywords: Alveolar soft part sarcoma, Chemotherapy, Child, Mouth floor, Tongue, Tracheotomy