November 2013 Vol. 1 No. 1

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Full Length Research Paper

Social impact of delayed male circumcision in a group of hemophiliacs’ patients from Sudan
 

S. E. Abdalla¹*, E. A. G. Khalil², F. A. M. Salih², M. M. H. Satti³, A. I. Basheer³, A. H. Elagib², A. A. Elnour², M. A. Ali⁴ and
I. F. Elmoola¹
 

¹Department of Pathology, Faculty of Medicine, Al Neelain University, Khartoum, Sudan.
²Institute of Endemic Diseases, University of Khartoum, Sudan.
³Department of Pathology, Faculty of Medicine, University of Khartoum, Sudan.
⁴Department of Urology, Khartoum Teaching Hospital, Sudan.

*Corresponding Author's E-mail: sanaseed@hotmail.com

Accepted October 30, 2013

Abstract

Haemophilia is the most common hereditary disorder of blood coagulation; there are two types, according to the factor deficient, haemophilia A in which there is factor VIII deficiency and haemophilia B with factor IX deficiency; and known as Christmas disease. In addition to life-long bleeding and other complications, a large number of haemophilics endure other sufferings. Social stigmatization, drug addiction, neglect, dropping out of school, loss of the father, these are only some of their problems. This prospective study was carried out on haemophilic patients who present themselves for circumcision, usually past the time for this procedure as compared to their peers. The studied aimed to critically assess and address the social problems that arise from delayed circumcision in male haemophilics in the Sudan. The study also assessed effect of circumcision on the problems of the individuals. The guardians/patients were enlightened about their disease and the surgical operation that was going to be performed. Following informed consent by guardians of the children or the children themselves if they are older than 18 years of age, a pre-designed questionnaire was filled by interviewers. In addition to demographic data, the questionnaire also contained detailed medical and treatment histories. The surgical operation was performed under factor concentrate cover according to the Sudanese National Haempphilia protocol and using cautery knife to minimize the chance of post-operative bleeding. 87 patients with haemophilia were enrolled in the study, 82 with haemophilia A and 5 with haemophilia B. The mean age of 12.8±5.6 year. The post-operative period went smoothly, apart from manageable breakthrough bleeding in three patients. All haemophiliacs and their families consider that circumcision is a very important and as a mandatory procedure.

Keywords: Factor eight, coagulation, partial thromboplastin time, bleeding, X-chromosome, hereditary